Recalcitrant steroid-resistant EGPA with multisystem involvement
نویسندگان
چکیده
منابع مشابه
Children with Steroid-resistant Nephrotic Syndrome: a Single-Center Study
Background and Aim: Steroid-resistant nephrotic syndrome (SRNS) accounts for 10%-20% of all cases of idiopathic nephrotic syndrome. These patients are at risk of developing end-stage renal disease. The aim of this study was to determine the demographic characteristics, renal biopsy findings, response to immunosuppressive treatment, and prognosis in pediatric patients with SRNS.Materials and Met...
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BACKGROUND The classical forms of severe SMA type 0 is well recognised by Pediatricians. CASE CHARACTERISTICS A hypotonic neonate with severe respiratory distress at birth. OBSERVATIONS Homozygous absence of exons 7 of the Survival Motor Neuron I gene. OUTCOME Died 108 days after admission when respiratory support was withdrawn at the request of the parents. MESSAGE Spinal Muscular Atro...
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A case of a 49-year-old male with exacerbation of eosinophilic granulomatosis with polyangiitis (EGPA) with heart involvement mimicking acute coronary syndrome is presented. Institution of intensive immunosupresive treatment resulted in the improvement of clinical condition and systolic left ventricular function. Coronary angiography excluded atherosclerosis as a primary cause of heart damage.
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ژورنال
عنوان ژورنال: Case Reports in Internal Medicine
سال: 2017
ISSN: 2332-7251,2332-7243
DOI: 10.5430/crim.v4n3p12